Stevens-Johnson syndrome (SJS) following switch to Nevirapine based regimen at Baylor-Uganda´s Paediatric Infectious Diseases Clinic, Mulago Hospital

Background: Nevirapine toxicities have previously been reported in especially older HIV infected females with high CD4s or recently improved immunity. This is a report on three patients managed at the Baylor -Uganda.
Methods: Medical records review.
Results: In the January 2009-2010 period, three patients aged: 13 years (male, initially on Combivir / Efavirenz but switched to Nevirapine due to excessive drowsiness at 96 weeks); a 22 year old (female, initially on Combivir / Efavirenz but switched to Nevirapine because of pregnancy) and a 9 years (female, initiated on Combivir / Nevirapine). Their CD4 cell counts prior to SJS were 24 % (447), 17 % (431), 15 % (335) for the 22, 13 and 9 years old respectively. About 2.5 weeks after starting Nevirapine, they all developed: high-grade fever, generalized itchy skin rash, swollen red eyes with photo phobia, and extensive oral sores. They were agitated, febrile, sore mouth, conjunctivitis, generalized erythematous maculopapular lesions which developed into vessiculobulous lessions and ulcers 1-3 days later. Laboratory investigations were fairly normal (alanine transaminases- 24, 52 and 52.3 U/l) except for raised Gamma-glutamyl transpeptidase (203.8, Normal range 0-60.0) in the 9year old and thrombocytosis (589x109/ ml) plus lymphocytosis (5.4%) in the 13 year old. All were hospitalized, HAART completely stopped, treated with intravenous fluids, antibiotics (ceftriaxone/ amoxyclav) for at least seven days and fed through a nasogastric tube for the 1-3 weeks hospital period. Steroids were administered in the initial 5 days of hospitalization, vitamin A given and saline wet gauze placed over the eyes to minimize eye damage according to the opthalmologist. They are stable on Nevirapine free HAART.
Conclusions: Stevens-Johnsons syndrome can present in HAART experienced stable children switching to a Nevirapine based regimen, therefore extra caution should be taken when switching and close followup done to detect and promptly manage reactions.

P. Kasirye Gitta1, S. Bakeera-Kitaka2, A. Kekitiinwa1
1Baylor Uganda (PIDC), Kampala, Uganda, 2Makarere University Medical School/Mulago Hospital, Paediatrics and Child Health, Kampala, Uganda